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The antibody against BCKDHB was raised in Rabbit using the recombinant fusion protein containing a sequence corresponding to amino acids 183-392 of human BCKDHB (NP_898871.1) as the immunogen. The polyclonal antibody exists as a isotype IgG, by affinity purification. This antibody has been validated on WB, ELISA.
The antibody against BCKDHB was raised in Rabbit using the recombinant fusion protein containing a sequence corresponding to amino acids 183-392 of human BCKDHB (NP_898871.1) as the immunogen. The polyclonal antibody exists as a isotype IgG, by affinity purification. This antibody has been validated on WB, ELISA.
| Cat.No | ADA-01617A | Clonality | Polyclonal |
|---|---|---|---|
| Host Species | Rabbit | Target Name | BCKDHB |
| Target Synonyms | E1B; BCKDE1B; BCKDH E1-beta; BCKDHB | Form | Liquid |
| Species Reactivity | Mouse, Rat | Isotype | IgG |
| Storage Buffer | 50% Glycerol, PBS with 0.02% sodium azide, pH7.3. | Purification Method | Affinity purification |
| Positive Samples | Mouse liver, Rat liver | Application | ELISA, WB |
| Immunogen Description | Recombinant fusion protein containing a sequence corresponding to amino acids 183-392 of human BCKDHB (NP_898871.1). | Target Species | Human |
|---|---|---|---|
| Uniprot ID | P21953 | Immunogen Sequence |
Uniprot Id
P21953
Target Species
Human
Target Name
BCKDHB
Target Full Name
2-oxoisovalerate dehydrogenase subunit beta, mitochondrial
Target Function
The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3).
Target Involvement
Maple syrup urine disease 1B (MSUD1B)
Target Subcellular Location
Mitochondrion matrix.
Target Synonyms
2 oxoisovalerate dehydrogenase subunit beta mitochondrial; 2-oxoisovalerate dehydrogenase subunit beta; mitochondrial; BCKDE1B; BCKDH E1-beta; BCKDHB; Branched chain alpha ketoacid dehydrogenase E1 beta subunit; Branched chain keto acid dehydrogenase E1 beta polypeptide ; Branched-chain alpha-keto acid dehydrogenase E1 component beta chain; dJ279A18.1; E1B; E1b beta subunit of the branched chain complex; FLJ17880; ODBB_HUMAN; RP1-279A18.1
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