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The antibody against L2HGDH was raised in rabbit using the Recombinant Human L-2-hydroxyglutarate dehydrogenase, mitochondrial protein (52-463AA) as the immunogen. This antibody exists as a non-conjugated isotype IgG, purified by protein G with a purity greater than 95%. This antibody has been validated on ELISA, WB, IHC.
The antibody against L2HGDH was raised in rabbit using the Recombinant Human L-2-hydroxyglutarate dehydrogenase, mitochondrial protein (52-463AA) as the immunogen. This antibody exists as a non-conjugated isotype IgG, purified by protein G with a purity greater than 95%. This antibody has been validated on ELISA, WB, IHC.
$299.00
| Cat.No | ADC-24601A | Clonality | Polyclonal |
|---|---|---|---|
| Host Species | Rabbit | Target Name | L2HGDH |
| Target Synonyms | mitochondrial antibody; L2HDH_HUMAN antibody; l2hgdh antibody; mitochondrial antibody | Form | Liquid |
| Species Reactivity | Human | Isotype | IgG |
| Storage Buffer | 0.01M PBS, 0.03% Proclin 300; Constituents: 50% Glycerol, PH 7.4 | Purification Method | >95%, Protein G purified |
| Conjugate | Non-conjugated | Application | ELISA, IHC, WB |
| Storage | Upon receipt |
| Immunogen Description | Recombinant Human L-2-hydroxyglutarate dehydrogenase, mitochondrial protein (52-463AA) | Target Species | Human |
|---|---|---|---|
| Immunogen Sequence | Complete sequences for the immunogen, target protein, and peptides are available upon request. | Uniprot ID | Q9H9P8 |
Uniprot Id
Q9H9P8
Target Species
Human
Target Name
L2HGDH
Target Full Name
L-2-hydroxyglutarate dehydrogenase, mitochondrial
Target Involvement
L-2-hydroxyglutaric aciduria (L2HGA)
Target Subcellular Location
Mitochondrion.
Target Protein Families
L2HGDH family
Target Tissue Specificity
Widely expressed. Highly expressed in brain, testis and muscle. Expressed to a lower extent in lymphocytes, fibroblasts, keratinocytes, placenta, bladder, small intestine, liver and bone marrow.
Target Research Area
Cell Biology
Target Synonyms
2 hydroxyglutarate dehydrogenase; Alpha hydroxyglutarate oxidoreductase; Alpha ketoglutarate reductase; C14orf160; Duranin; FLJ12618; L alpha hydroxyglutarate dehydrogenase; L-2-hydroxyglutarate dehydrogenase; L-2-hydroxyglutarate dehydrogenase, mitochondrial; L2HDH_HUMAN; l2hgdh; mitochondrial
Target Background
This gene encodes L-2-hydroxyglutarate dehydrogenase, a FAD-dependent enzyme that oxidizes L-2-hydroxyglutarate to alpha-ketoglutarate in a variety of mammalian tissues. Mutations in this gene cause L-2-hydroxyglutaric aciduria, a rare autosomal recessive neurometabolic disorder resulting in moderate to severe cognitive disability.
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