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Rabbit anti-Human ASL Polyclonal Antibody

The antibody against ASL was raised in rabbit using the Fusion protein of Human ASL as the immunogen. This antibody exists as a non-conjugated isotype IgG, Antigen affinity purified. This antibody has been validated on ELISA, IHC.

ADC-30872A

The antibody against ASL was raised in rabbit using the Fusion protein of Human ASL as the immunogen. This antibody exists as a non-conjugated isotype IgG, Antigen affinity purified. This antibody has been validated on ELISA, IHC.

$299.00

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Specifications


Cat.No ADC-30872A ClonalityPolyclonal
Host SpeciesRabbitTarget NameASL
Target SynonymsArgininosuccinase antibody; Argininosuccinate lyase antibody; Arginosuccinase antibody; ARLY_HUMAN antibody; ASAL antibody; ASL antibody; EC 4.3.2.1 antibodyFormLiquid
Species ReactivityHuman, Mouse, RatIsotypeIgG
Storage Buffer0.05% NaN3, 40% Glycerol., pH7.4 PBSPurification MethodAntigen affinity purified
ConjugateNon-conjugatedApplicationELISA, IHC
StorageUpon receipt

Immunogen Information


Immunogen DescriptionFusion protein of Human ASLTarget SpeciesHuman
Immunogen SequenceComplete sequences for the immunogen, target protein, and peptides are available upon request.Uniprot IDP04424
Background Information
  • Uniprot Id

    P04424

  • Target Species

    Human

  • Target Name

    ASL

  • Target Full Name

    Argininosuccinate lyase

  • Target Involvement

    Argininosuccinic aciduria (ARGINSA)

  • Target Protein Families

    Lyase 1 family, Argininosuccinate lyase subfamily

  • Target Synonyms

    Argininosuccinase; Argininosuccinate lyase; Arginosuccinase; ARLY_HUMAN; ASAL; ASL; EC 4.3.2.1

  • Target Background

    This gene encodes a member of the lyase 1 family. The encoded protein forms a cytosolic homotetramer and primarily catalyzes the reversible hydrolytic cleavage of argininosuccinate into arginine and fumarate, an essential step in the liver in detoxifying ammonia via the urea cycle. Mutations in this gene result in the autosomal recessive disorder argininosuccinic aciduria, or argininosuccinic acid lyase deficiency. A nontranscribed pseudogene is also located on the long arm of chromosome 22. Alternatively spliced transcript variants encoding different isoforms have been described.

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