Chinese (Simplified)
English
German
Korean
Spanish
Sign up for an account to enjoy easy online shopping and instant order tracking.
The antibody against BOLA3 was raised in rabbit using the Recombinant Human BolA-like protein 3 protein (1-79AA) as the immunogen. This antibody exists as a non-conjugated isotype IgG, purified by protein G with a purity greater than 95%. This antibody has been validated on ELISA, IHC.
The antibody against BOLA3 was raised in rabbit using the Recombinant Human BolA-like protein 3 protein (1-79AA) as the immunogen. This antibody exists as a non-conjugated isotype IgG, purified by protein G with a purity greater than 95%. This antibody has been validated on ELISA, IHC.
$299.00
Immunohistochemistry of paraffin-embedded human kidney tissue using BOLA3 Antibody at dilution of 1:100
| Cat.No | ADC-13778A | Clonality | Polyclonal |
|---|---|---|---|
| Host Species | Rabbit | Target Name | BOLA3 |
| Target Synonyms | BolA-like protein 3 antibody; BOLA3 antibody; BOLA3_HUMAN antibody; MMDS2 antibody | Form | Liquid |
| Species Reactivity | Human | Isotype | IgG |
| Storage Buffer | 0.01M PBS, 0.03% Proclin 300; Constituents: 50% Glycerol, PH 7.4 | Purification Method | >95%, Protein G purified |
| Conjugate | Non-conjugated | Application | ELISA, IHC |
| Storage | Upon receipt |
| Immunogen Description | Recombinant Human BolA-like protein 3 protein (1-79AA) | Target Species | Human |
|---|---|---|---|
| Immunogen Sequence | Complete sequences for the immunogen, target protein, and peptides are available upon request. | Uniprot ID | Q53S33 |
Uniprot Id
Q53S33
Target Species
Human
Target Name
BOLA3
Target Full Name
BolA-like protein 3
Target Function
Acts as a mitochondrial iron-sulfur (Fe-S) cluster assembly factor that facilitates (Fe-S) cluster insertion into a subset of mitochondrial proteins. Probably acts together with NFU1.
Target Involvement
Multiple mitochondrial dysfunctions syndrome 2 with hyperglycinemia (MMDS2)
Target Subcellular Location
Mitochondrion.
Target Protein Families
BolA/IbaG family
Target Tissue Specificity
Widely expressed.
Target Synonyms
BolA-like protein 3; BOLA3; BOLA3_HUMAN; MMDS2
Target Background
This gene encodes a protein that plays an essential role in the production of iron-sulfur (Fe-S) clusters for the normal maturation of lipoate-containing 2-oxoacid dehydrogenases, and for the assembly of the mitochondrial respiratory chain complexes. Mutation in this gene has been associated with multiple mitochondrial dysfunctions syndrome-2. Two alternatively spliced transcript variants encoding different isoforms with distinct subcellular localization have been reported for this gene (PMID:21944046).
Free shipping on orders $999+
Advenit post multos Scudilo Scutariorum tribunus velament
We accept credit cards, PayPal, and bank wires
Responsive and knowledgable customer service via email, text or phone
Notification
