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Rabbit anti-Human CLN6 Polyclonal Antibody

The antibody against CLN6 was raised in rabbit using the Synthesized peptide derived from the C-terminal region of Human CLN6. as the immunogen. This antibody exists as a non-conjugated isotype IgG. The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen. This antibody has been validated on WB, IHC, ELISA.

ADC-34602A

The antibody against CLN6 was raised in rabbit using the Synthesized peptide derived from the C-terminal region of Human CLN6. as the immunogen. This antibody exists as a non-conjugated isotype IgG. The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen. This antibody has been validated on WB, IHC, ELISA.

$167.00

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Specifications


Cat.No ADC-34602A ClonalityPolyclonal
Host SpeciesRabbitTarget NameCLN6
Target SynonymsCLN6; Ceroid-lipofuscinosis neuronal protein 6; Protein CLN6FormLiquid
Species ReactivityHumanIsotypeIgG
Storage Buffer0.5% BSA and 0.02% sodium azide., Liquid in PBS containing 50% glycerolPurification MethodThe antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
ConjugateNon-conjugatedApplicationELISA, IHC, WB
StorageUpon receipt

Immunogen Information


Immunogen DescriptionSynthesized peptide derived from the C-terminal region of Human CLN6.Target SpeciesHuman
Immunogen SequenceComplete sequences for the immunogen, target protein, and peptides are available upon request.Uniprot IDQ9NWW5
Background Information
  • Uniprot Id

    Q9NWW5

  • Target Species

    Human

  • Target Name

    CLN6

  • Target Full Name

    Ceroid-lipofuscinosis neuronal protein 6

  • Target Involvement

    Ceroid lipofuscinosis, neuronal, 6 (CLN6); Ceroid lipofuscinosis, neuronal, 4A (CLN4A)

  • Target Subcellular Location

    Endoplasmic reticulum membrane; Multi-pass membrane protein. Endoplasmic reticulum.

  • Target Synonyms

    CLN6; Ceroid-lipofuscinosis neuronal protein 6; Protein CLN6

  • Target Background

    This gene is one of eight which have been associated with neuronal ceroid lipofuscinoses (NCL). Also referred to as Batten disease, NCL comprises a class of autosomal recessive, neurodegenerative disorders affecting children. The genes responsible likely encode proteins involved in the degradation of post-translationally modified proteins in lysosomes. The primary defect in NCL disorders is thought to be associated with lysosomal storage function.

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